Hemangioma related to Maffucci syndrome in a man: a case report
نویسنده
چکیده
INTRODUCTION Maffucci syndrome is a rare clinical entity (approximately 200 cases have been reported in the medical literature) with a combined occurrence of multiple enchondromas and vascular tumors. CASE PRESENTATION The case of a 43-year-old Japanese man with multiple chondromas and hemangiomas (Maffucci syndrome) is reported. One of the hemangiomas was removed and examined pathologically. The morphological picture was an admixture of cavernous hemangioma and spindle cell hemangioma without cytological atypia or mitosis. Sheets of vacuolated endothelial cells were also observed. CONCLUSION A rare case of hemangioma associated with Maffucci syndrome, focusing on the pathologic nature of the submitted tissue, is reported.
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معرفی یک بیمار مبتلا به سندرم مافوچی
Introduction: Maffucci syndrome is a rare clinical entity (approximately 200 cases have been reported in the medical literature) with a combination occurrence of multiple enchodroma and vascular tumors. Case Report: Our patient was an 18 year old girl born in a non-consanguineous marriage with finger and toe bones disorders (enchondroma) causing deformity of fingers and toes with multiple vas...
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